GNS anticorps (C-Term)

N° du produit ABIN928079

L’anticorps Lapin Polyclonal anti-GNS a été validé pour WB. Il convient pour détecter GNS dans des échantillons de Humain et Rat.

Aperçu rapide pour GNS anticorps (C-Term) (ABIN928079)

Antigène: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Reactivité: Humain, Rat

Hôte: Lapin

Clonalité: Polyclonal

Conjugué: Cet anticorp GNS est non-conjugé

Application: Western Blotting (WB)

Détail du produit anti-GNS anticorps

Épitope: C-Term

Réactivité croisée: Rat (Rattus)

Purification: Purified

Immunogène: Gns antibody was raised in rabbit using the C terminal of Gns as the immunogen

Information d'application

Indications d'application: WB: 0.2-1 µg/mL
Optimal conditions should be determined by the investigator.

Commentaires:

Gns Blocking Peptide, (ABIN936100), is also available for use as a blocking control in assays to test for specificity of this Gns antibody

Restrictions: For Research Use only

Stockage

Format: Lyophilized

Concentration: Lot specific

Buffer: Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.

Conseil sur la manipulation: Avoid repeated freeze/thaw cycles.

Stock: 4 °C/-20 °C

Stockage commentaire: Store at 4 °C, following reconstitution, aliquot and store at -20 °C.

Détails sur GNS

Antigène: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Autre désignation: Gns

Sujet: GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. Synonyms: Polyclonal Gns antibody, Anti-Gns antibody, glucosamine, N-acetyl-6-sulfatase antibody, Gns antibody.

Pathways: Glycosaminoglycan Metabolic Process